CASE REPORT

Combined Non-Syndromic Coronal-Lambdoid Craniosynostosis: a challenging diagnosis

Craniossinostose Combinada Coronal-Lambdoide Não Sindrômica: diagnóstico desafiador

  • Tatiana Protzenko 1    Tatiana Protzenko 1
  • Clara Magalhães 1    Clara Magalhães 1
  • Marcelo Pousa 1    Marcelo Pousa 1
  • Antônio Bellas 1    Antônio Bellas 1
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  Downloads: 26

Resumo

Craniossinostose multissutural não sindrômica não é comum, especialmente aquelas que envolvem suturas coronais e lambdoides unilaterais. Com base em um relato de caso, discutimos a morfologia do crânio na sinostose combinada da sutura coronal-lambdoide unilateral, os desafios para realizar o diagnóstico e o tratamento cirúrgico adequado.

Palavras-chave

Plagiocefalia anterior; Plagiocefalia posterior; Craniossinostose combinada; Plagiocefalia posicional; Craniossinostose não sindrômica

Abstract

Nonsyndromic, multi-suture craniosynostosis is not common, especially those involving unilateral coronal and lambdoid sutures. Based on a case report, we discussed the morphology of the skull of combined unilateral coronal-lambdoid suture synostosis, the challenges to perform diagnosis and appropriate surgical treatment.


Keywords

Anterior plagiocephaly; Posterior plagiocephaly; Combined craniosynostosis; Positional plagiocephaly; Nonsyndromic craniosynostosis

References

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1Instituto Nacional de Saúde da Mulher, da Criança e do Adolescente Fernandes Figueira, Fundação Oswaldo Cruz – Fiocruz, Rio de Janeiro, RJ, Brasil.

 

Received Apr 5, 2024

Accepted June 10, 2024

JBNC  Brazilian Journal of Neurosurgery

JBNC
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  •   e-ISSN (online version): 2446-6786
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